Anatomical segment/connection:
Atrial morphology and arrangement
Example of pathology
Situs inversus
Left/right atrial isomerism
Juxtaposition of atrial appendages
Cot-triatriatum
Anatomical segment/connection:
Pulmonary or systemic venous connection
Example of pathology
Complete/partial abnormal pulmonary venous connection, persistent left superior caval vein with or without absent right superior caval vein, pulmonary or systemic vein stenoses
Anatomical segment/connection:
Interatrial septum
Example of pathology
Atrial septal defect
Patent foramen ovale
Aneurysm
Pouch
Anatomical segment/connection:
Atrio-ventricular connection and relation
Example of pathology
Atrio-ventricular discordance (ventricular inversion)
Double inlet
Criss-cross heart
Supero-inferior ventricles
Anatomical segment/connection:
Atrio-ventricular valves
Example of pathology
Cleft
Double orifice
Additional valve tissue
Parachute mitral valve
Hypoplasia
Dysplasia
Stenosis
Atresia
Straddling
Overriding
Ebstein anomaly
Anatomical segment/connection:
Interventricular septum
Example of pathology
Ventricular septal defect
Anatomical segment/connection:
Ventricular outflow tract
Example of pathology
Left — tunnel, discrete subvalvular obstruction
Right — double chambered right ventricle
Anatomical segment/connection:
Ventriculo-arterial connection
Example of pathology
Transposition
Double outlet
Common arterial trunk
Anatomical segment/connection:
Great arteries
Example of pathology
Valvular pathology
Supravalvular obstruction
Patent arterial duct
Aortopulmonary window
Major aortopulmonary collateral arteries (MAPCAS)
Anatomical segment/connection:
Coronary arteries
Example of pathology
Abnormal origin
Fistulas