Anatomical segment/connection: Atrial morphology and arrangement |
| Example of pathology |
| Situs inversus |
| Left/right atrial isomerism |
| Juxtaposition of atrial appendages |
| Cot-triatriatum |
Anatomical segment/connection: Pulmonary or systemic venous connection |
| Example of pathology |
| Complete/partial abnormal pulmonary venous connection, persistent left superior caval vein with or without absent right superior caval vein, pulmonary or systemic vein stenoses |
Anatomical segment/connection: Interatrial septum |
| Example of pathology |
| Atrial septal defect |
| Patent foramen ovale |
| Aneurysm |
| Pouch |
Anatomical segment/connection: Atrio-ventricular connection and relation |
| Example of pathology |
| Atrio-ventricular discordance (ventricular inversion) |
| Double inlet |
| Criss-cross heart |
| Supero-inferior ventricles |
Anatomical segment/connection: Atrio-ventricular valves |
| Example of pathology |
| Cleft |
| Double orifice |
| Additional valve tissue |
| Parachute mitral valve |
| Hypoplasia |
| Dysplasia |
| Stenosis |
| Atresia |
| Straddling |
| Overriding |
| Ebstein anomaly |
Anatomical segment/connection: Interventricular septum |
| Example of pathology |
| Ventricular septal defect |
Anatomical segment/connection: Ventricular outflow tract |
| Example of pathology |
| Left — tunnel, discrete subvalvular obstruction |
| Right — double chambered right ventricle |
Anatomical segment/connection: Ventriculo-arterial connection |
| Example of pathology |
| Transposition |
| Double outlet |
| Common arterial trunk |
Anatomical segment/connection: Great arteries |
| Example of pathology |
| Valvular pathology |
| Supravalvular obstruction |
| Patent arterial duct |
| Aortopulmonary window |
| Major aortopulmonary collateral arteries (MAPCAS) |
Anatomical segment/connection: Coronary arteries |
| Example of pathology |
| Abnormal origin |
| Fistulas |